PREVALENCE OF SELECTED
IMMUNODEFICIENCY DISEASES
DISEASE WORLDWIDE
PREVALENCE
IgA immunodeficiency 1:700
Hereditary angioedema
(deficiency in C1 inhibitor)*
1:1000
Common variable
hypogammaglobulinemia
1:70,000
Severe combined immunodeficiency
disease (SCID)--all forms
1:100,000
X-linked agammglobulinemia 1:200,000
* Complement deficiences are discussed in Chapter 14.