| PREVALENCE OF SELECTED IMMUNODEFICIENCY DISEASES | ||
| DISEASE | WORLDWIDE PREVALENCE | |
| IgA immunodeficiency | 1:700 | |
| Hereditary angioedema (deficiency in C1 inhibitor)* | 1:1000 | |
| Common variable hypogammaglobulinemia | 1:70,000 | |
| Severe combined immunodeficiency disease (SCID)--all forms | 1:100,000 | |
| X-linked agammglobulinemia | 1:200,000 | |
| * Complement deficiences are discussed in Chapter 14. | ||