| PREVALENCE OF SELECTED IMMUNODEFICIENCY DISEASES |
||
| DISEASE | WORLDWIDE PREVALENCE |
|
| IgA immunodeficiency | 1:700 | |
| Hereditary angioedema (deficiency in C1 inhibitor)* |
1:1000 | |
| Common variable hypogammaglobulinemia |
1:70,000 | |
| Severe combined immunodeficiency disease (SCID)--all forms |
1:100,000 | |
| X-linked agammglobulinemia | 1:200,000 | |
| * Complement deficiences are discussed in Chapter 14. | ||